Long QT syndrome: from channels to cardiac arrhythmias.
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ABSTRACT:
SUBMITTER: Moss AJ
PROVIDER: S-EPMC1180552 | biostudies-literature | 2005 Aug
REPOSITORIES: biostudies-literature
Publications
Long QT syndrome: from channels to cardiac arrhythmias.
Moss Arthur J AJ Kass Robert S RS
The Journal of clinical investigation 20050801 8
Long QT syndrome, a rare genetic disorder associated with life-threatening arrhythmias, has provided a wealth of information about fundamental mechanisms underlying human cardiac electrophysiology that has come about because of truly collaborative interactions between clinical and basic scientists. Our understanding of the mechanisms that control the critical plateau and repolarization phases of the human ventricular action potential has been raised to new levels through these studies, which hav ...[more]
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