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The neuralgic amyotrophy consultation.

ABSTRACT: Neuralgic amyotrophy is a distinct clinical syndrome with acute severe pain and patchy paresis in the shoulder and arm region. The clinical phenotype was recently found to be more comprehensive and the long-term prognosis less optimistic than usually assumed for many patients. The disorder can be idiopathic or hereditary in an autosomal dominant fashion, with only few phenotypical variations between the two. This article provides a practical overview of current knowledge on the clinical presentation, diagnosis, pathogenesis and the treatment of pain and complications.

SUBMITTER: van Alfen N

PROVIDER: S-EPMC2780663 | biostudies-literature | 2007 Jun

REPOSITORIES: biostudies-literature

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The neuralgic amyotrophy consultation.

van Alfen Nens N

Journal of neurology 20070420 6

Neuralgic amyotrophy is a distinct clinical syndrome with acute severe pain and patchy paresis in the shoulder and arm region. The clinical phenotype was recently found to be more comprehensive and the long-term prognosis less optimistic than usually assumed for many patients. The disorder can be idiopathic or hereditary in an autosomal dominant fashion, with only few phenotypical variations between the two. This article provides a practical overview of current knowledge on the clinical presenta ...[more]

PMID: 17446996

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Project description: Not available

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