Ontology highlight
ABSTRACT:
SUBMITTER: Schaefer IM
PROVIDER: S-EPMC3843285 | biostudies-literature | 2013
REPOSITORIES: biostudies-literature
Schaefer Inga-Marie IM Ströbel Philipp P Thiha Aung A Sohns Jan Martin JM Mühlfeld Christian C Küffer Stefan S Felmerer Gunther G Stepniewski Adam A Pauli Silke S Agaimy Abbas A
International journal of clinical and experimental pathology 20131115 12
Perineurioma is a rare benign peripheral nerve sheath tumor featuring perineurial differentiation. Perineurioma occurs sporadically with only one reported case in the setting of neurofibromatosis type 1 (NF-1). We present a 6.7-cm soft tissue perineurioma of the lower leg in a 51-year-old man with proven NF-1. The tumor displayed whorled and fascicular pattern with infiltrative margins and expressed EMA, GLUT-1, claudin-1, and CD34. Electron microscopy confirmed diagnosis. Furthermore, lipomatos ...[more]