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Achondroplasia with oligodontia: Report of a rare case.

ABSTRACT: Achondroplasia is considered as a form of skeletal dysplasia/dwarfism that manifests with stunted stature and disproportionate limb shortening. Achondroplasia is of special interest in the field of dentistry because of its characteristic craniofacial features. It has been considered as the most common short-limbed dwarfism syndrome. Very few authors have reported the presence of oligodontia in achondroplastic patients. The present paper reports a rare case of oligodontia in a young, female, achondroplastic patient.

SUBMITTER: Kale L

PROVIDER: S-EPMC3927355 | biostudies-literature | 2013 Sep

REPOSITORIES: biostudies-literature

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Achondroplasia with oligodontia: Report of a rare case.

Kale Lata L Khambete Neha N Sodhi Sonia S Kumar Rahul R

Journal of oral and maxillofacial pathology : JOMFP 20130901 3

Achondroplasia is considered as a form of skeletal dysplasia/dwarfism that manifests with stunted stature and disproportionate limb shortening. Achondroplasia is of special interest in the field of dentistry because of its characteristic craniofacial features. It has been considered as the most common short-limbed dwarfism syndrome. Very few authors have reported the presence of oligodontia in achondroplastic patients. The present paper reports a rare case of oligodontia in a young, female, acho ...[more]

PMID: 24574672

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