Ontology highlight
ABSTRACT:
SUBMITTER: Poziomczyk CS
PROVIDER: S-EPMC3938351 | biostudies-literature | 2014 Jan-Feb
REPOSITORIES: biostudies-literature
Anais brasileiros de dermatologia 20140101 1
Incontinentia pigmenti is a rare genodermatosis in which the skin involvement occurs in all patients. Additionally, other ectodermal tissues may be affected, such as the central nervous system, eyes, hair, nails and teeth. The disease has a X-linked dominant inheritance pattern and is usually lethal to male fetuses. The dermatological findings occur in four successive phases, following the lines of Blaschko: First phase - vesicles on an erythematous base; second phase - verrucous hyperkeratotic ...[more]