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Total anomalous systemic venous drainage with heterotaxia syndrome: a rare case.

ABSTRACT: Total anomalous systemic venous return is a very rare anomaly, where vena cava inferior, vena cava superior, and coronary sinus drain into left atrium. Two-day-old male baby was admitted with cyanosis and tachypnea after the birth. Left atrial isomerism with anomalous systemic venous drainage was found on echocardiographic examination. We present an unusual case of total anomalous systemic venous drainage in to the left atrium.

SUBMITTER: Yildirim A

PROVIDER: S-EPMC4145383 | biostudies-literature | 2014

REPOSITORIES: biostudies-literature

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Total anomalous systemic venous drainage with heterotaxia syndrome: a rare case.

Yildirim Ali A Kosger Pelin P Ozdemir Gokmen G Ucar Birsen B Kilic Zubeyir Z

Case reports in cardiology 20140812

Total anomalous systemic venous return is a very rare anomaly, where vena cava inferior, vena cava superior, and coronary sinus drain into left atrium. Two-day-old male baby was admitted with cyanosis and tachypnea after the birth. Left atrial isomerism with anomalous systemic venous drainage was found on echocardiographic examination. We present an unusual case of total anomalous systemic venous drainage in to the left atrium. ...[more]

PMID: 25197579

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