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Right ventricular cavity near obliteration in neonatal severe biventricular hypertrophic cardiomyopathy.


ABSTRACT: A newborn presenting with cyanosis at day 9 of life was admitted to the local hospital. Initial local echocardiography confirmed a cardiac issue and the patient was transferred to a tertiary cardiac hospital. Further imaging confirmed a rare presentation of cardiomyopathy with severe right ventricular outflow tract obstruction. Surgery was performed but with postoperative haemodynamic instability complicated by incessant ventricular tachycardia. Following discussion with the family, care was withdrawn. Postmortem demonstrated a rare form of hypertrophic cardiomyopathy with right ventricular outflow tract obstruction not previously described in a neonate.

SUBMITTER: Jivanji SG 

PROVIDER: S-EPMC4208136 | biostudies-literature | 2014 Oct

REPOSITORIES: biostudies-literature

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Right ventricular cavity near obliteration in neonatal severe biventricular hypertrophic cardiomyopathy.

Jivanji Salim G M SG   Daubeney Piers P   Franklin Rodney R   Sheppard Mary M  

BMJ case reports 20141021


A newborn presenting with cyanosis at day 9 of life was admitted to the local hospital. Initial local echocardiography confirmed a cardiac issue and the patient was transferred to a tertiary cardiac hospital. Further imaging confirmed a rare presentation of cardiomyopathy with severe right ventricular outflow tract obstruction. Surgery was performed but with postoperative haemodynamic instability complicated by incessant ventricular tachycardia. Following discussion with the family, care was wit  ...[more]

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