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Anesthetic and dental management of a child with IMAGe syndrome.

ABSTRACT: IMAGe syndrome (OMIM 300290) is a rare multisystem disorder that has a broad phenotypic presentation. Though variable, this disorder mainly consists of Intrauterine growth retardation, Metaphyseal dysplasia, Adrenal hypoplasia congenita, and Genital abnormalities. Patients with IMAGe syndrome present as an uncommon yet important challenge for dentists and anesthesiologists due to their wide range of dysmorphic facial features, adrenal insufficiency, electrolyte imbalances, and need for steroid replacement. The purpose of this case report is to describe the successful anesthetic management of a pediatric patient diagnosed with IMAGe syndrome who presented for full mouth dental rehabilitation.

SUBMITTER: Lindemeyer RG

PROVIDER: S-EPMC4269357 | biostudies-literature | 2014

REPOSITORIES: biostudies-literature

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Anesthetic and dental management of a child with IMAGe syndrome.

Lindemeyer Rochelle G RG Rashewsky Stephanie E SE Louie Phillip J PJ Schleelein Laura L

Anesthesia progress 20140101 4

IMAGe syndrome (OMIM 300290) is a rare multisystem disorder that has a broad phenotypic presentation. Though variable, this disorder mainly consists of Intrauterine growth retardation, Metaphyseal dysplasia, Adrenal hypoplasia congenita, and Genital abnormalities. Patients with IMAGe syndrome present as an uncommon yet important challenge for dentists and anesthesiologists due to their wide range of dysmorphic facial features, adrenal insufficiency, electrolyte imbalances, and need for steroid r ...[more]

PMID: 25517553

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