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An extremely rare cause of Eisenmenger syndrome.

ABSTRACT: Persistent Truncus Arteriosus (PTA) is an extremely rare defect accounting for under 1% of all congenital heart disease, and over 85% of patients succumb to heart failure in infancy. We report a case of van Praagh type A3 PTA, which represents its rarest variant and accounts for only 8-10% of all patients with PTA. The presence of ductal stenosis in such cases is further exceedingly rare.

SUBMITTER: Phadke MS

PROVIDER: S-EPMC4310993 | biostudies-literature | 2014 Nov-Dec

REPOSITORIES: biostudies-literature

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An extremely rare cause of Eisenmenger syndrome.

Phadke Milind S MS Sabnis Girish R GR Patil Devendra V DV Lanjewar Charan P CP Kerkar Prafulla G PG

Indian heart journal 20141105 6

Persistent Truncus Arteriosus (PTA) is an extremely rare defect accounting for under 1% of all congenital heart disease, and over 85% of patients succumb to heart failure in infancy. We report a case of van Praagh type A3 PTA, which represents its rarest variant and accounts for only 8-10% of all patients with PTA. The presence of ductal stenosis in such cases is further exceedingly rare. ...[more]

PMID: 25634421

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