Primary ectopic frontotemporal craniopharyngioma.
Ontology highlight
ABSTRACT: Introduction
Primary ectopic craniopharyngiomas have only rarely been reported. Craniopharyngiomas involve usually the sellar and suprasellar region, but can be originated from cell remnants of the obliterated craniopharyngeal duct or metaplastic change of andenohypophyseal cells. We present the first case of a primary ectopic frontotemporal craniopharyngioma.Presentation of case
A 35-year old woman presented with a one-year history of headache and diplopia. MRI showed a large frontotemporal cystic lesion. Tumor resection was performed with a keyhole endoscopic frontal lateral approach. The pathological features showed an adamantinomatous craniopharyngioma with a cholesterol granuloma reaction.Discussion
There have been reported different localizations for primary ectopic craniopharyngioma. Our case presented a lobulated frontotemporal cystic mass formed by a dense eosinophilic proteinaceous material dystrophic calcifications and cholesterol crystals, with epithelial remnants. No tumor regrowth was observed in the magnetic resonance image 27 months postoperatively.Conclusion
Primary ectopic craniopharyngioma is a rare entity with a pathogenesis that remains uncertain. This is an unusual anatomic location associated with unique clinical findings.
SUBMITTER: Ortega-Porcayo LA
PROVIDER: S-EPMC4392184 | biostudies-literature | 2015
REPOSITORIES: biostudies-literature
Publications
Primary ectopic frontotemporal craniopharyngioma.
Ortega-Porcayo Luis Alberto LA Ponce-Gómez Juan Antonio JA Martínez-Moreno Mauricio M Portocarrero-Ortíz Lesly L Tena-Suck Martha Lilia ML Gómez-Amador Juan Luis JL
International journal of surgery case reports 20150108
<h4>Introduction</h4>Primary ectopic craniopharyngiomas have only rarely been reported. Craniopharyngiomas involve usually the sellar and suprasellar region, but can be originated from cell remnants of the obliterated craniopharyngeal duct or metaplastic change of andenohypophyseal cells. We present the first case of a primary ectopic frontotemporal craniopharyngioma.<h4>Presentation of case</h4>A 35-year old woman presented with a one-year history of headache and diplopia. MRI showed a large fr ...[more]
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