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Isolation of the right subclavian artery in a patient with d-transposition of the great arteries.

ABSTRACT: Isolation of the right subclavian artery (RSCA) is rare, and this finding in association with d-transposition of the great arteries (d-TGA) is extremely unusual. We present a case of an isolated RSCA in a newborn with d-TGA in whom the clinical presentation was diagnostic. We discuss the imaging modalities used to confirm the diagnosis, the embryological basis of the finding, and the surgical repair.

SUBMITTER: Arunamata A

PROVIDER: S-EPMC4453190 | biostudies-literature | 2015 May-Aug

REPOSITORIES: biostudies-literature

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Isolation of the right subclavian artery in a patient with d-transposition of the great arteries.

Arunamata Alisa A Perry Stanton B SB Kipps Alaina K AK Vasanawala Shreyas S SS Axelrod David M DM

Annals of pediatric cardiology 20150501 2

Isolation of the right subclavian artery (RSCA) is rare, and this finding in association with d-transposition of the great arteries (d-TGA) is extremely unusual. We present a case of an isolated RSCA in a newborn with d-TGA in whom the clinical presentation was diagnostic. We discuss the imaging modalities used to confirm the diagnosis, the embryological basis of the finding, and the surgical repair. ...[more]

PMID: 26085773

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