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Unicuspid unicommissural aortic valve: an extremely rare congenital anomaly.

ABSTRACT: Unicuspid aortic valve is a rare congenital malformation that usually presents in the 3rd to 5th decade of life-and usually with severe aortic stenosis or regurgitation. It often requires surgical correction. Diagnosis can be made with 2- or 3-dimensional transthoracic or transesophageal echocardiography, cardiac computed tomography, or cardiac magnetic resonance imaging. We report the case of a 31-year-old man who presented with dyspnea on exertion due to severe aortic stenosis secondary to a unicuspid unicommissural aortic valve. After aortic valve replacement, this patient experienced complete heart block that required the placement of a permanent pacemaker.

SUBMITTER: Singh S

PROVIDER: S-EPMC4473628 | biostudies-literature | 2015 Jun

REPOSITORIES: biostudies-literature

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Unicuspid unicommissural aortic valve: an extremely rare congenital anomaly.

Singh Sukhjeet S Ghayal Puneet P Mathur Atish A Mysliwiec Margaret M Lovoulos Constantinos C Solanki Pallavi P Klapholz Marc M Maher James J

Texas Heart Institute journal 20150601 3

Unicuspid aortic valve is a rare congenital malformation that usually presents in the 3rd to 5th decade of life-and usually with severe aortic stenosis or regurgitation. It often requires surgical correction. Diagnosis can be made with 2- or 3-dimensional transthoracic or transesophageal echocardiography, cardiac computed tomography, or cardiac magnetic resonance imaging. We report the case of a 31-year-old man who presented with dyspnea on exertion due to severe aortic stenosis secondary to a u ...[more]

PMID: 26175647

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