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Blastic plasmacytoid dendritic cell neoplasm (BPDCN): a rare entity.

ABSTRACT: Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare and aggressive haematological malignancy in the elderly, with a high frequency of cutaneous and bone marrow involvement and poor prognosis. We report a case of BPDCN with classic presentation and discuss its treatment and the value of different investigation tools used in diagnosis and response assessment.

SUBMITTER: Lim MS

PROVIDER: S-EPMC4735436 | biostudies-literature | 2016 Jan

REPOSITORIES: biostudies-literature

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Blastic plasmacytoid dendritic cell neoplasm (BPDCN): a rare entity.

Lim Ming Sheng MS Lemmert Karla K Enjeti Anoop A

BMJ case reports 20160120

Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare and aggressive haematological malignancy in the elderly, with a high frequency of cutaneous and bone marrow involvement and poor prognosis. We report a case of BPDCN with classic presentation and discuss its treatment and the value of different investigation tools used in diagnosis and response assessment. ...[more]

PMID: 26791132

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