Reversible man-in-the-barrel syndrome in myasthenia gravis.
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ABSTRACT:
SUBMITTER: Shah PA
PROVIDER: S-EPMC4782563 | biostudies-literature | 2016 Jan-Mar
REPOSITORIES: biostudies-literature
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Reversible man-in-the-barrel syndrome in myasthenia gravis.
Shah Poornima A PA Wadia Pettarusp Murzban PM
Annals of Indian Academy of Neurology 20160101 1
Man-in-the-barrel syndrome (MBS) is an uncommon presentation due to bilateral, predominantly proximal muscle weakness that has not been described to be associated with myasthenia gravis. We describe a case of myasthenia gravis presenting as MBS. Additionally, he had significant wasting of the deltoids bilaterally with fibrillations on electromyography (EMG) at rest and brief duration (3-6 ms) bi/triphasic motor unit potentials (MUPs) on submaximal effort apart from a decremental response on repe ...[more]
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