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Role of perioperative transesophageal echocardiography in the management of adolescent truncus arteriosus: rare case report.

ABSTRACT: Truncus arteriosus (TA) is a rare congenital heart disease defined as a single arterial vessel arising from the heart that gives origin to the systemic, pulmonary and coronary circulations. The truncal valve in majority of the cases is tricuspid though quadricuspid and bicuspid valves have been reported. Patients with TA typically have a large nonrestrictive sub truncal ventricular septal defect. Survival of these infants beyond 1-year is uncommon. Here, we report a unique case of 12-year-old female patient with persistent TA who underwent surgical repair by using transesophageal echocardiography as a monitoring device during the perioperative management.

SUBMITTER: Nagaraja PS

PROVIDER: S-EPMC4881631 | biostudies-literature | 2015 Apr-Jun

REPOSITORIES: biostudies-literature

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Role of perioperative transesophageal echocardiography in the management of adolescent truncus arteriosus: rare case report.

Nagaraja P S PS Singh Naveen G NG Simha Parimala Prasanna PP Davan K R KR Manjunath V V Jagadeesh A M AM

Annals of cardiac anaesthesia 20150401 2

Truncus arteriosus (TA) is a rare congenital heart disease defined as a single arterial vessel arising from the heart that gives origin to the systemic, pulmonary and coronary circulations. The truncal valve in majority of the cases is tricuspid though quadricuspid and bicuspid valves have been reported. Patients with TA typically have a large nonrestrictive sub truncal ventricular septal defect. Survival of these infants beyond 1-year is uncommon. Here, we report a unique case of 12-year-old fe ...[more]

PMID: 25849699

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