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Ollier disease with anaplastic astrocytoma: A review of the literature and a unique case.

ABSTRACT: BACKGROUND:Ollier disease is a rare, nonfamilial disorder that primary affects the long bones and cartilage of joints with multiple enchondromas. It is associated with a higher risk of central nervous system (CNS) malignancies; although the incidence is unknown. CASE DESCRIPTION:Here, we present the case of a 55-year-old woman who developed an anaplastic astrocytoma with a known diagnosis of Ollier disease with a survival time of over 3 years. CONCLUSION:This report draws attention to the rarity of this disease and the paucity of information regarding CNS involvement in Ollier disease, as well as reviews the current literature.

SUBMITTER: Gajavelli S

PROVIDER: S-EPMC5025950 | biostudies-literature | 2016

REPOSITORIES: biostudies-literature

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Ollier disease with anaplastic astrocytoma: A review of the literature and a unique case.

Gajavelli Srikanth S Nakhla Jonathan J Nasser Rani R Yassari Reza R Weidenheim Karen M KM Graber Jerome J

Surgical neurology international 20160901 Suppl 23

<h4>Background</h4>Ollier disease is a rare, nonfamilial disorder that primary affects the long bones and cartilage of joints with multiple enchondromas. It is associated with a higher risk of central nervous system (CNS) malignancies; although the incidence is unknown.<h4>Case description</h4>Here, we present the case of a 55-year-old woman who developed an anaplastic astrocytoma with a known diagnosis of Ollier disease with a survival time of over 3 years.<h4>Conclusion</h4>This report draws a ...[more]

PMID: 27656320

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