Mounier-Kuhn syndrome: a case of tracheal smooth muscle remodeling.
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ABSTRACT:
SUBMITTER: Cook DP
PROVIDER: S-EPMC5290513 | biostudies-literature | 2017 Feb
REPOSITORIES: biostudies-literature
Publications
Mounier-Kuhn syndrome: a case of tracheal smooth muscle remodeling.
Cook Daniel P DP Adam Ryan J RJ Abou Alaiwa Mahmoud H MH Eberlein Michael M Klesney-Tait Julia A JA Parekh Kalpaj R KR Meyerholz David K DK Stoltz David A DA
Clinical case reports 20161229 2
Mounier-Kuhn syndrome is a rare clinical disorder characterized by tracheobronchial dilation and recurrent lower respiratory tract infections. While the etiology of the disease remains unknown, histopathological analysis of Mounier-Kuhn airways demonstrates that the disease is, in part, characterized by cellular changes in airway smooth muscle. ...[more]
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