Limb Amputation after Multiple Treatments of Tenosynovial Giant Cell Tumour: Series of 4 Dutch Cases.
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SUBMITTER: Mastboom MJL
PROVIDER: S-EPMC5506462 | biostudies-literature | 2017
REPOSITORIES: biostudies-literature
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Limb Amputation after Multiple Treatments of Tenosynovial Giant Cell Tumour: Series of 4 Dutch Cases.
Mastboom Monique J L MJL Verspoor Floortje G M FGM Gelderblom Hans H van de Sande Michiel A J MAJ
Case reports in orthopedics 20170628
In Tenosynovial Giant Cell Tumours (TGCT), previously named Pigmented Villonodular Synovitis (PVNS), a distinction is made between a single nodule (localized-type) and multiple nodules (diffuse-type). Diffuse-type is considered locally aggressive. Onset and extermination of this orphan disease remain unclear. Surgical resection is the most commonly performed treatment. Unfortunately, recurrences often occur (up to 92%), necessitating reoperations and adjuvant treatments. Once all treatments fail ...[more]
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