Ontology highlight
ABSTRACT:
SUBMITTER: Di Monaco S
PROVIDER: S-EPMC5983654 | biostudies-literature | 2018 May
REPOSITORIES: biostudies-literature
Di Monaco Silvia S Georges Adrien A Lengelé Jean-Philippe JP Vikkula Miikka M Persu Alexandre A
International journal of molecular sciences 20180521 5
Fibromuscular Dysplasia (FMD) is “an idiopathic, segmental, non-atherosclerotic and non-inflammatory disease of the musculature of arterial walls, leading to stenosis of small and medium-sized arteries” (Persu, et al; 2014). FMD can lead to hypertension, arterial dissections, subarachnoid haemorrhage, stroke or mesenteric ischemia. The pathophysiology of the disease remains elusive. While familial cases are rare (<5%) in contemporary FMD registries, there is evidence in favour of the ...[more]