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Pedunculated and obstructive Wilms' tumor: A rare presentation in a 2 year-old male.

ABSTRACT: Wilms' tumor manifesting as an obstructing ureteral mass is extremely rare. Herein, we report an unusual case in which a child presented with a clinical picture concerning for and suggestive of ureteropelvic junction obstruction (UPJO), but was instead found to have an intrapelvic pedunculated Wilms' tumor with extension into the proximal ureter. We discuss the patient's diagnostic workup, radiographic, operative and pathologic findings, as well as important lessons learned from this unusual case.

SUBMITTER: Arbel LT

PROVIDER: S-EPMC6008277 | biostudies-literature | 2018 Sep

REPOSITORIES: biostudies-literature

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Pedunculated and obstructive Wilms' tumor: A rare presentation in a 2 year-old male.

Arbel Leor T LT Jessop Morris M Al-Omar Osama O

Urology case reports 20180607

Wilms' tumor manifesting as an obstructing ureteral mass is extremely rare. Herein, we report an unusual case in which a child presented with a clinical picture concerning for and suggestive of ureteropelvic junction obstruction (UPJO), but was instead found to have an intrapelvic pedunculated Wilms' tumor with extension into the proximal ureter. We discuss the patient's diagnostic workup, radiographic, operative and pathologic findings, as well as important lessons learned from this unusual cas ...[more]

PMID: 29928591

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