Dataset Information

On-Top-Plasty for Atypical Thumb Duplication: A Case Report With 10 Year Follow-up.

ABSTRACT:

Background

A very uncommon pattern of thumb duplication consists of an ulnar-side floating thumb and a radial-side distally hypoplastic thumb.

Methods

We report the case of a 15-month-old child with this type of thumb duplication on his right hand treated with an on-top-plasty technique. The ulnar-side segment was pedicled and transferred to the lateral thumb, which was distally resected.

Results

A well-aligned and widely mobile thumb with a wide first web and an excellent cosmetic appearance was exhibited 10 years after surgery.

Conclusions

On-top-plasty technique might be amenable to reconstruct certain atypical thumb duplications.

SUBMITTER: Pons-Riverola A

PROVIDER: S-EPMC6081786 | biostudies-literature | 2018 Jul

REPOSITORIES: biostudies-literature

ACCESS DATA

Publications

On-Top-Plasty for Atypical Thumb Duplication: A Case Report With 10 Year Follow-up.

Pons-Riverola Albert A Camprubi-Garcia Eric E Barrera-Ochoa Sergi S Bergua-Domingo Josep M JM Knorr Jorge J Soldado Francisco F

Hand (New York, N.Y.) 20180422 4

<h4>Background</h4>A very uncommon pattern of thumb duplication consists of an ulnar-side floating thumb and a radial-side distally hypoplastic thumb.<h4>Methods</h4>We report the case of a 15-month-old child with this type of thumb duplication on his right hand treated with an on-top-plasty technique. The ulnar-side segment was pedicled and transferred to the lateral thumb, which was distally resected.<h4>Results</h4>A well-aligned and widely mobile thumb with a wide first web and an excellent ...[more]

PMID: 29682986

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Project description:Sotos syndrome is caused by a gene deletion with an autosomal dominant pattern of inheritance. Cerebral gigantism, hypotonia and joint hyperextensibility are characteristic features of this syndrome. A percentage of these patients develop progressive scoliosis early in life. In the literature, few studies on the evolution of scoliosis in Sotos syndrome have been published. We retrospectively evaluated eight patients diagnosed with Sotos syndrome and scoliosis treated at the Garrahan Children Hospital between 1988 and March 2009. Clinical charts and imaging studies were assessed. Eight patients (19%) presented with scoliosis and seven of them (87.5%) required surgical treatment. The mean follow-up was 9.5 years (range 3-18). Mean age at first consultation was 5.2 years (range 1.1-11.2). Mean Cobb angle for scoliosis at first consultation was 34.3° (range 20°-42°) and the mean Cobb angle for kyphosis was 45.6° (range 30°-90°). Mean age at surgery was 11.2 years (range 3.7-18.10). The surgical procedures performed were instrumented posterior arthrodesis, alone or combined with anterior arthrodesis, instrumented anterior arthrodesis, while one patient is currently in treatment with growing rods. Preoperative mean Cobb angle for scoliosis was 72.3° (range 54°-130°) and for kyphosis was 59.8° (range 30°-108°); postoperative mean Cobb angle for scoliosis was 45.5° (range 6°-90°) and for kyphosis was 40.2° (range 30°-80°). There were three early complications (pleural effusion in two cases and death due to sepsis in one) and two late complications (kyphosis above the instrumentation area and dislodgement of the proximal hooks). Incidence of scoliosis in Sotos syndrome is high and thus close monitoring of patients with Sotos syndrome during growth is important for early detection of this entity. Joint hyperextensibility and hypotonia that are characteristic of the syndrome should be considered at the moment of surgery to avoid short fusions.

Dataset Information

On-Top-Plasty for Atypical Thumb Duplication: A Case Report With 10 Year Follow-up.

Background

Methods

Results

Conclusions

Publications

On-Top-Plasty for Atypical Thumb Duplication: A Case Report With 10 Year Follow-up.

Similar Datasets

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