Post-partum catastrophic antiphospholipid syndrome presenting with shock and digital ischaemia - A diagnostic and management challenge.
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ABSTRACT:
SUBMITTER: Sadick V
PROVIDER: S-EPMC6259081 | biostudies-literature | 2018 Nov
REPOSITORIES: biostudies-literature
Publications
Post-partum catastrophic antiphospholipid syndrome presenting with shock and digital ischaemia - A diagnostic and management challenge.
Sadick Victoria V Lane Stuart S Fischer Eddy E Seppelt Ian I Shetty Anita A McLean Anthony A
Journal of the Intensive Care Society 20180319 4
Catastrophic antiphospholipid syndrome is a rare multisystem autoimmune condition characterised by rapid development of widespread thrombotic disease and subsequent multi-organ failure. It is the most severe complication of antiphospholipid syndrome, carrying significant morbidity and mortality. We report a patient with post-partum catastrophic antiphospholipid syndrome with cardiac, hepatic, renal and cutaneous manifestations. The diagnostic challenges in establishing a definitive diagnosis in ...[more]
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