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Long-term follow-up of an adult with left pulmonary artery stenting and absent right pulmonary artery: a case report.

ABSTRACT:

Background

Unilateral absence of pulmonary artery is a rare congenital abnormality with varied clinical presentations. We present a unique case of congenital absence of right pulmonary artery (RPA) with left pulmonary artery (LPA) origin stenosis without any intracardiac or extracardiac lesion and its long-term follow-up.

Case summary

A 68-year-old woman underwent successful LPA stenting 23?years back for absent RPA and LPA origin stenosis. She was recently evaluated for breathlessness, almost two decades after the procedure. On evaluation, she was found to have severe pulmonary hypertension (Group 5) without any distortion of the LPA and with normally functioning stent.

Discussion

This report discusses the long-term outcome of stenting in the setting of severe stenosis of a single pulmonary artery. Over the years, the patient went on to develop severe segmental pulmonary hypertension (Group 5).

SUBMITTER: Sharma B

PROVIDER: S-EPMC6439359 | biostudies-literature | 2019 Mar

REPOSITORIES: biostudies-literature

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Long-term follow-up of an adult with left pulmonary artery stenting and absent right pulmonary artery: a case report.

Sharma Bharti B Dalvi Bharat V BV

European heart journal. Case reports 20190220 1

<h4>Background</h4>Unilateral absence of pulmonary artery is a rare congenital abnormality with varied clinical presentations. We present a unique case of congenital absence of right pulmonary artery (RPA) with left pulmonary artery (LPA) origin stenosis without any intracardiac or extracardiac lesion and its long-term follow-up.<h4>Case summary</h4>A 68-year-old woman underwent successful LPA stenting 23 years back for absent RPA and LPA origin stenosis. She was recently evaluated for breathles ...[more]

PMID: 31020257

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