Dataset Information

Hemi Masticatory Spasm: Series of 7 Cases and Review of Literature.

ABSTRACT:

Background

Hemi masticatory spasm (HMS) is a rare movement disorder affecting muscles of mastication attributed to dysfunction of motor branch of trigeminal nerve and is characterized by painful spasm of masticatory muscles. Microvascular compression leading to focal demyelination of motor branch of trigeminal nerve is the most speculated on mechanism of HMS. Treatment options range from medical to surgical approaches, but botulinm toxin (BTX) has now become the preferred treatment.

Cases

We report a retrospective review of 7 cases of HMS, supported by electrophysiological and clinical findings. All the cases had excellent response to BTX therapy.

Discussion and conclusion

In this article, we highlight the delay in diagnosis of HMS attributed to rarity, long course of illness, association with hemiatrophy, "Lichen Sclerosus et Atrophicus," and scleroderma/morphea. Considering the favorable outcome to BTXs, surgical treatment can be avoided or delayed in majority except secondary cases.

SUBMITTER: Radhakrishnan DM

PROVIDER: S-EPMC6476625 | biostudies-literature | 2019 Apr

REPOSITORIES: biostudies-literature

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Publications

Hemi Masticatory Spasm: Series of 7 Cases and Review of Literature.

Radhakrishnan Divya M DM Goyal Vinay V Shukla Garima G Singh Mamta Bhushan MB Ramam M M

Movement disorders clinical practice 20190404 4

<h4>Background</h4>Hemi masticatory spasm (HMS) is a rare movement disorder affecting muscles of mastication attributed to dysfunction of motor branch of trigeminal nerve and is characterized by painful spasm of masticatory muscles. Microvascular compression leading to focal demyelination of motor branch of trigeminal nerve is the most speculated on mechanism of HMS. Treatment options range from medical to surgical approaches, but botulinm toxin (BTX) has now become the preferred treatment.<h4>C ...[more]

PMID: 31061840

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Dataset Information

Hemi Masticatory Spasm: Series of 7 Cases and Review of Literature.

Background

Cases

Discussion and conclusion

Publications

Hemi Masticatory Spasm: Series of 7 Cases and Review of Literature.

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