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Delayed Propriospinal Myoclonus Following Dorsal Spinal Cord Surgery.

ABSTRACT: Cerebral disorders are known to be associated with myoclonus, but spinal pathologies have received little attention as a causative factor in movement disorders. Propriospinal myoclonus (PSM) is a rare hyperkinetic movement disorder caused by activity of a spinal pattern generator localized in a few segments of the spinal cord, spreading to other intraspinal segments via propriospinal pathways. Majority of cases of PSM are reported as functional movement disorders. Structural lesions were found in only a small number of reported cases. We present this rare case report of a patient who developed PSM 2 years following spinal surgery, done 5 years ago for D6-D7 vertebral body collapse. To the best of our knowledge, only few cases of PSM have been reported after spinal surgery and none from India.

SUBMITTER: Sardana V

PROVIDER: S-EPMC6839301 | biostudies-literature | 2019 Oct-Dec

REPOSITORIES: biostudies-literature

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Delayed Propriospinal Myoclonus Following Dorsal Spinal Cord Surgery.

Sardana Vijay V Sharma Sunil Kumar SK

Annals of Indian Academy of Neurology 20191025 4

Cerebral disorders are known to be associated with myoclonus, but spinal pathologies have received little attention as a causative factor in movement disorders. Propriospinal myoclonus (PSM) is a rare hyperkinetic movement disorder caused by activity of a spinal pattern generator localized in a few segments of the spinal cord, spreading to other intraspinal segments via propriospinal pathways. Majority of cases of PSM are reported as functional movement disorders. Structural lesions were found i ...[more]

PMID: 31736579

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