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Management of ruptured sinus of valsalva for device closure in a patient with haemophilia.

ABSTRACT: The association of Hemophilia A and ruptured aneurysm of sinus of valsalva (RSOV) has never been reported to the best of our knowledge. We report the case of a 29-year-old male patient with Hemophilia type A who presented with a RSOV into right atrium (RA). The patient underwent device closure off the RSOV and received Factor VIII infusions to decrease blood loss. The peri-procedural management is being presented in this case report.

SUBMITTER: Dhawan I

PROVIDER: S-EPMC7034198 | biostudies-literature | 2020 Jan-Mar

REPOSITORIES: biostudies-literature

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Management of ruptured sinus of valsalva for device closure in a patient with haemophilia.

Dhawan Ira I Choudhury Arindam A Aggarwal Shivani S Chauhan Sandeep S

Annals of cardiac anaesthesia 20200101 1

The association of Hemophilia A and ruptured aneurysm of sinus of valsalva (RSOV) has never been reported to the best of our knowledge. We report the case of a 29-year-old male patient with Hemophilia type A who presented with a RSOV into right atrium (RA). The patient underwent device closure off the RSOV and received Factor VIII infusions to decrease blood loss. The peri-procedural management is being presented in this case report. ...[more]

PMID: 31929254

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