Ectopic ACTH Secretion in a Child With Metastatic Ewing's Sarcoma: A Case Report.
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ABSTRACT:
SUBMITTER: Di Ruscio V
PROVIDER: S-EPMC7198717 | biostudies-literature | 2020
REPOSITORIES: biostudies-literature
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Ectopic ACTH Secretion in a Child With Metastatic Ewing's Sarcoma: A Case Report.
Di Ruscio Valentina V Del Baldo Giada G De Pasquale Maria Debora MD De Vito Rita R Miele Evelina E Colafati Giovanna Stefania GS Deodati Annalisa A De Ioris Maria Antonietta MA Tornesello Assunta A Milano Giuseppe Maria GM Mastronuzzi Angela A
Frontiers in oncology 20200428
Ectopic ACTH syndrome is rare in pediatric age. Sarcomas that cause Ectopic ACTH Syndrome (EAS) are even more uncommon. Currently, only three cases of EAS caused by Ewing' sarcoma have been reported. We detail a 10-year-old boy with Cushing's syndrome symptoms caused by ectopic ACTH production by a metastatic Ewing's sarcoma of the right ischio-pubic and ileo-pubic branches. The rapid appearance of cushingoid symptoms, with significant weight gain, acne, hirsutism, and hypercortisolism were impl ...[more]
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