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Dermoscopy of Follicular Dowling-Degos Disease.

ABSTRACT: Dowling-Degos disease (DDD) is a late-onset genodermatosis characterized by hyperpigmented macules on the flexures along with scattered comedo-like lesions and pitted acneiform scars. Follicular Dowling-Degos is a rare type of DDD, with only two reports so far. It presents with follicular papules and comedo-like lesions predominantly on the face and trunk. Dermoscopy of follicular DDD shows irregular star-shaped/Chinese letter pattern pigmentation along with comedo-like lesions. Herein, we describe diagnostic clues including dermoscopy in three patients of follicular DDD which can help in differentiating it from other disorders presenting with comedo-like lesions.

SUBMITTER: Dabas G

PROVIDER: S-EPMC7423220 | biostudies-literature | 2020 Jul-Aug

REPOSITORIES: biostudies-literature

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Dermoscopy of Follicular Dowling-Degos Disease.

Dabas Garima G Mahajan Rahul R Afra T P TP De Dipankar D Handa Sanjeev S Aggarwal Divya D Radotra Bishan Das BD

Indian journal of dermatology 20200701 4

Dowling-Degos disease (DDD) is a late-onset genodermatosis characterized by hyperpigmented macules on the flexures along with scattered comedo-like lesions and pitted acneiform scars. Follicular Dowling-Degos is a rare type of DDD, with only two reports so far. It presents with follicular papules and comedo-like lesions predominantly on the face and trunk. Dermoscopy of follicular DDD shows irregular star-shaped/Chinese letter pattern pigmentation along with comedo-like lesions. Herein, we descr ...[more]

PMID: 32831370

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