Transthyretin amyloid cardiomyopathy: An uncharted territory awaiting discovery.
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ABSTRACT:
SUBMITTER: Porcari A
PROVIDER: S-EPMC7534738 | biostudies-literature | 2020 Dec
REPOSITORIES: biostudies-literature
Publications
Transthyretin amyloid cardiomyopathy: An uncharted territory awaiting discovery.
Porcari Aldostefano A Merlo Marco M Rapezzi Claudio C Sinagra Gianfranco G
European journal of internal medicine 20201005
Transthyretin amyloid cardiomyopathy (ATTR-AC) is an under-recognized and underdiagnosed disease. Although traditionally considered a rare condition, the epidemiology of the disease is rapidly changing due to the possibility of non-invasive diagnosis through cardiac scintigraphy with bone tracers and novel disease-modifying treatments providing survival advantages. Nevertheless, many questions and grey areas have to be addressed, such as the natural history of ATTR-AC, the role and implications ...[more]
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