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Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise.

ABSTRACT: Pulmonary artery intimal sarcoma (PAIS) is a very rare tumour. The prevalence of PAIS is estimated to be between 0.001% and 0.003%, but this may be an underestimation because of potential misdiagnosis due to its similar presentation to that of pulmonary thromboembolism. The prognosis is very poor, with median overall survival between 11 and 18 months. We report a case of a 36-year-old man who presented to our cardiac surgery clinic reporting nonspecific symptoms and was found to have PAIS requiring surgical resection and adjuvant chemotherapy. We outline the radiologic features, pathologic characteristics, surgical approach, and chemotherapy treatment utilized.

SUBMITTER: Rabbani M

PROVIDER: S-EPMC7710993 | biostudies-literature | 2020 Nov

REPOSITORIES: biostudies-literature

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Pulmonary Artery Intimal Sarcoma: A Deadly Diagnosis in Disguise.

Rabbani Mohamad M Hafiz Ahmed A Algadheeb Muhanad M Tugaleva Elena E Bergin Margaret Lynn ML Ray Guo Lin-Rui LR

CJC open 20200717 6

Pulmonary artery intimal sarcoma (PAIS) is a very rare tumour. The prevalence of PAIS is estimated to be between 0.001% and 0.003%, but this may be an underestimation because of potential misdiagnosis due to its similar presentation to that of pulmonary thromboembolism. The prognosis is very poor, with median overall survival between 11 and 18 months. We report a case of a 36-year-old man who presented to our cardiac surgery clinic reporting nonspecific symptoms and was found to have PAIS requir ...[more]

PMID: 33305235

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