Dataset Information

Sclerosing pneumocytoma in a 1-year-old girl presenting with massive hemoptysis: A case report.

ABSTRACT:

Introduction and importance

Sclerosing pneumocytoma (SP) is a rare benign neoplasm of the lung with peak age incidence in middle aged-women. Here we report, for the first time in the literature, a case of a 1-year-old girl with SP.

Case presentation

A 1-year-old girl was reported to emergency department for massive hemoptysis. After admission, the patient had a three-days episode of melena, with normal body temperature and generally stable condition.

Clinical discussion

Fiberoptic bronchoscopy was normal. MSCT was done along with angiography and Three-Dimensional Reconstruction which revealed a well-circumscribed round mass with well-defined borders located near the vessels in the upper lobe of left lung. Anatomic lingula resection was performed. Hilar node was also resected. The histopathological examination confirmed the presence of SP. Fourteen months postoperatively, the patient was in a good health with no clinical or radiological evidence of recurrence.

Conclusion

SP is a rare benign tumor which usually presents in middle aged-women asymptomatically or with nonspecific symptoms. We report this case to highlight that SP should be considered in cases of hemoptysis in young children.

SUBMITTER: Bara A

PROVIDER: S-EPMC7806499 | biostudies-literature | 2021 Feb

REPOSITORIES: biostudies-literature

ACCESS DATA

Publications

Sclerosing pneumocytoma in a 1-year-old girl presenting with massive hemoptysis: A case report.

Bara Albaraa A Adham Ibrahim I Daaboul Obada O Aldimirawi Fatima F Darwish Bassam B Haffar Lina L

Annals of medicine and surgery (2012) 20210108

<h4>Introduction and importance</h4>Sclerosing pneumocytoma (SP) is a rare benign neoplasm of the lung with peak age incidence in middle aged-women. Here we report, for the first time in the literature, a case of a 1-year-old girl with SP.<h4>Case presentation</h4>A 1-year-old girl was reported to emergency department for massive hemoptysis. After admission, the patient had a three-days episode of melena, with normal body temperature and generally stable condition.<h4>Clinical discussion</h4>Fib ...[more]

PMID: 33489116

Similar Datasets

Project description:Introduction and importance Pulmonary sclerosing pneumocytoma (PSP) is a rare tumor thought to originate from respiratory epithelial cells. It is usually benign, but may rarely metastasize to lymph nodes. Surgeons face unique challenges in diagnosis and management of this condition, and ideal surgical management is yet to be established. Case presentation 48-year-old woman with a 7 × 7 mm pulmonary lesion discovered incidentally on computerized tomography (CT) imaging, which grew to 9 mm over the following year. Seven years later, follow-up imaging revealed that the mass had grown to 1.3 cm in largest dimension. Surgery was recommended and the mass was resected via a right video-assisted thoracic surgery (VATS) middle lobectomy with mediastinal lymph node dissection. All lymph nodes were negative and the patient's postoperative course was unremarkable. Clinical discussion There are few evidence-based guidelines available on the treatment and postoperative surveillance of PSP. Research has shown comparable recurrence-free survival rates for sublobar resection and lobectomy, though recurrence can occur, especially following sublobar resection in larger or more centrally-located tumors. In absence of established guidelines, it was decided to follow this patient according to NCCN guidelines for surveillance of early-stage non-small cell lung cancer due to potential risk of recurrence. Conclusion This case report adds to the limited literature on PSP and depicts a possible treatment and postoperative follow-up plan. Right VATS middle lobectomy can effectively treat some cases of central PSP. In absence of established guidelines for postoperative follow-up of PSP, NCCN guidelines may outline one possible strategy for postoperative management. Highlights • Pulmonary sclerosing pneumocytoma presents diagnostic and therapeutic challenges.• Right VATS lobectomy is an effective treatment for some cases of PSP.• There is no established protocol to follow cases of PSP postoperatively.• NCCN guidelines may provide a potential postoperative surveillance plan.

Dataset Information

Sclerosing pneumocytoma in a 1-year-old girl presenting with massive hemoptysis: A case report.

Introduction and importance

Case presentation

Clinical discussion

Conclusion

Publications

Sclerosing pneumocytoma in a 1-year-old girl presenting with massive hemoptysis: A case report.

Similar Datasets

OmicsDI is part of the ELIXIR infrastructure

Tweets