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Case Report: A Rare Case of Right-Sided Papillary Fibroelastoma in a 1-Year-Old With Congenital Heart Disease.

ABSTRACT: Introduction: Cardiac papillary fibroelastomas (PFEs) are the most common primary benign cardiac tumors, although they are somewhat unusual in children and typically seen on the left-sided cardiac valves. Case summary: A 10-week-old patient was found to have a partial atrioventricular canal defect, with associated tricuspid and mitral regurgitation. He was medically managed until 1 year of age, when surgical correction was done. During the procedure, a PFE was found incidentally on the TV. Conclusion: This is one of the youngest patients to be reported with PFE, thus adding to the literature of these unusual cases in children.

SUBMITTER: Ahmad A

PROVIDER: S-EPMC7873290 | biostudies-literature | 2020

REPOSITORIES: biostudies-literature

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Case Report: A Rare Case of Right-Sided Papillary Fibroelastoma in a 1-Year-Old With Congenital Heart Disease.

Ahmad Ali A El-Am Edward A EA Kurmann Reto D RD Hagler Donald J DJ Bois Melanie C MC Maleszewski Joseph J JJ Klarich Kyle W KW

Frontiers in cardiovascular medicine 20210127

<b>Introduction:</b> Cardiac papillary fibroelastomas (PFEs) are the most common primary benign cardiac tumors, although they are somewhat unusual in children and typically seen on the left-sided cardiac valves. <b>Case summary:</b> A 10-week-old patient was found to have a partial atrioventricular canal defect, with associated tricuspid and mitral regurgitation. He was medically managed until 1 year of age, when surgical correction was done. During the procedure, a PFE was found incidentally on ...[more]

PMID: 33585585

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Two Rare Manifestations of Cardiac Papillary Fibroelastoma Presenting with Dyspnea.

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Extremely rare rapid development of a papillary fibroelastoma on the left ventricular anterior papillary muscle.

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2020-06-04 | GSE151766 | GEO

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