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Intrahepatic intraductal papillary cystic neoplasm of the bile duct: A case report.


ABSTRACT:

Introduction and importance

Intraductal papillary neoplasm of the bile duct (IPNB) is a tumour with a very low incidence in the Western world, characterised by a high risk of malignant transformation and unknown prognosis. It is a new entity which was adopted by the WHO in 2010 as a precursor lesion of cholangiocarcinoma. Intrahepatic bile duct is the most common site of origin for IPNB.

Case presentation

Hereby, we present a case of an asymptomatic 63- year-old man, referred to our department after routine ultrasonography showing a multifocal cystic lesion on the left hepatic lobe. Further screening modalities (CT, MRI abdo) confirmed a complex cystic liver lesion with atypical features. The patient underwent left hepatectomy. Histopathology showed a cystic type intrahepatic IPNB, which was completely resected (R0). The follow up in 2 yrs post-operation showed no signs of recurrence.

Clinical discussion

The diagnosis and management of IPNB remain challenging. A multimodality imaging approach is essential in order to diagnose IPNB, assess tumour location and extent and plan the optimal treatment strategy.

Conclusion

Complete surgical resection (R0) with close postoperative follow-up offers long-term survival.

SUBMITTER: Baltagiannis EG 

PROVIDER: S-EPMC7900680 | biostudies-literature | 2021 Mar

REPOSITORIES: biostudies-literature

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Intrahepatic intraductal papillary cystic neoplasm of the bile duct: A case report.

Baltagiannis Evangelos G EG   Kalyvioti Christina C   Glantzouni Anastasia A   Batistatou Anna A   Tzimas Petros P   Glantzounis Georgios K GK  

Annals of medicine and surgery (2012) 20210212


<h4>Introduction and importance</h4>Intraductal papillary neoplasm of the bile duct (IPNB) is a tumour with a very low incidence in the Western world, characterised by a high risk of malignant transformation and unknown prognosis. It is a new entity which was adopted by the WHO in 2010 as a precursor lesion of cholangiocarcinoma. Intrahepatic bile duct is the most common site of origin for IPNB.<h4>Case presentation</h4>Hereby, we present a case of an asymptomatic 63- year-old man, referred to o  ...[more]

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