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Rare case of huge vulvar angiomyofibroblastoma in a young female.

ABSTRACT: Mesenchymal tumours of the vulva are rare and consist of two types, difficult to distinguish but with different prognoses. Angiomyofibroblastoma (AMFB) is a benign tumour, whereas Aggressive Angiomyxoma (AA) is an infiltrating tumour. We describe a 22-year-old nulliparous patient with a vulvar mass sized 19 cm in diameter. After preoperative assessment by ultrasound, chest X-ray, and MRI, wide excision on the tumour was done and diagnosed as AMFB. Differentiation from AA is being discussed.

SUBMITTER: Anggraeni TD

PROVIDER: S-EPMC8040263 | biostudies-literature | 2021 May

REPOSITORIES: biostudies-literature

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Rare case of huge vulvar angiomyofibroblastoma in a young female.

Anggraeni Tricia Dewi TD Nuranna Laila L Luthfiyanto Muhammad M Siregar Nuryati Chairani NC Hellyanti Tantri T Siregar Trifonia Pingkan TP Alexandra Leonardo L

Gynecologic oncology reports 20210322

Mesenchymal tumours of the vulva are rare and consist of two types, difficult to distinguish but with different prognoses. Angiomyofibroblastoma (AMFB) is a benign tumour, whereas Aggressive Angiomyxoma (AA) is an infiltrating tumour. We describe a 22-year-old nulliparous patient with a vulvar mass sized 19 cm in diameter. After preoperative assessment by ultrasound, chest X-ray, and MRI, wide excision on the tumour was done and diagnosed as AMFB. Differentiation from AA is being discussed. ...[more]

PMID: 33869711

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