Unknown

Dataset Information

0

Retropharyngeal chordoma extending to the spinal cord, mimicking a neurogenic tumor: a case report and literature review.


ABSTRACT: Chordomas are rare, locally aggressive bone malignancies with poor prognoses. However, those with minimal or no bone involvement are more easily resectable because of their well-delineated margins and thus have better prognoses. Such extraosseous chordomas of the spine are localized both intradurally and extradurally. Only a few case reports have focused on extraosseous, extradural spinal chordomas. Radiologically, this type of chordoma has a dumbbell shape; however, dumbbell-shaped spinal tumors are traditionally thought to be neurogenic tumors (i.e., schwannomas or neurofibromas). We herein report a unique case involving a woman with a dumbbell-shaped extraosseous chordoma protruding predominantly into the retropharyngeal space. A 44-year-old woman presented for evaluation of a left submandibular mass. A T2-hyperintense, gadolinium-enhancing mass was found in her cervical spinal canal, protruding through the C2/3 neural foramen into the retropharyngeal space with minimal vertebral involvement. The initial diagnosis was a neurogenic tumor, most likely a schwannoma. After subtotal removal, the pathologic diagnosis was a chordoma. Because chordomas and schwannomas have significantly different prognoses, caution is warranted when a dumbbell-shaped tumor is identified in the spine with minimal or no vertebral deterioration on radiology. This report also provides the first thorough review of extraosseous dumbbell-shaped intraspinal-extraspinal chordomas.

SUBMITTER: Lee SJ 

PROVIDER: S-EPMC8166386 | biostudies-literature |

REPOSITORIES: biostudies-literature

Similar Datasets

| S-EPMC5548420 | biostudies-other
| S-EPMC6998794 | biostudies-literature
| S-EPMC9457049 | biostudies-literature
| S-EPMC4665336 | biostudies-literature
| S-EPMC6505757 | biostudies-literature
| S-EPMC7026187 | biostudies-literature
| S-EPMC4078123 | biostudies-other
2015-07-13 | E-GEOD-64891 | biostudies-arrayexpress
2015-07-13 | GSE64891 | GEO
| S-EPMC5690745 | biostudies-literature