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Granulomatosis with polyangiitis (Wegener's) complicated by splenic rupture and severe acute respiratory distress syndrome: A case report.


ABSTRACT: Even in the absence of disease-specific radiological signs of granulomatosis with polyangiitis (GPA), severe intrapulmonary GPA may be present. Rapidly establishing the diagnosis with a confirmatory biopsy is key to initiate lifesaving therapy.

SUBMITTER: Ahmad Y 

PROVIDER: S-EPMC8271247 | biostudies-literature |

REPOSITORIES: biostudies-literature

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