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Membranous septal aneurysm in a child with Noonan syndrome and hypertrophic cardiomyopathy.

ABSTRACT: A 4-year-old boy was diagnosed with hypertrophic cardiomyopathy with moderate degree of obstruction of the left ventricular outflow tract, secondary to asymmetric septal hypertrophy during infancy. Echocardiogram on follow-up showed increase in left ventricular outflow tract obstruction and appearance of an aneurysm in the membranous portion of interventricular septum. The appearance of the membranous septal aneurysm may be related to the direction of jet arising from the point of contact of the anterior mitral leaflet with the hypertrophied basal septum and hitting this part of the interventricular septum.

Supplementary information

The online version contains supplementary material available at 10.1007/s12055-021-01287-x.

SUBMITTER: Arunakumar P

PROVIDER: S-EPMC9218020 | biostudies-literature | 2022 Jul

REPOSITORIES: biostudies-literature

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Membranous septal aneurysm in a child with Noonan syndrome and hypertrophic cardiomyopathy.

Arunakumar Priyadarshini P Sastry Usha Mk UM Satyamurthy Ramya Guddekeri RG Jayaranganath M

Indian journal of thoracic and cardiovascular surgery 20220117 4

A 4-year-old boy was diagnosed with hypertrophic cardiomyopathy with moderate degree of obstruction of the left ventricular outflow tract, secondary to asymmetric septal hypertrophy during infancy. Echocardiogram on follow-up showed increase in left ventricular outflow tract obstruction and appearance of an aneurysm in the membranous portion of interventricular septum. The appearance of the membranous septal aneurysm may be related to the direction of jet arising from the point of contact of the ...[more]

PMID: 35756553

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