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Portocaval paraganglioma: A second case report

ABSTRACT:

Study design

Case Report.

Introduction and importance

To report a case of a paraganglioma presenting in an uncommon location in the abdomen.

Case presentation

A 24-year-old man with an abdominal lesion presented with one-year history of severe headaches and palpitations.

Interventions and outcome

The tumor was surgically resected and was later diagnosed as an extra-adrenal paraganglioma.

Conclusion

The unique location of a paraganglioma could prove misleading, making it easier to confuse it with other malignant lesions, but it still can't be excluded, and with proper techniques it can be surgically excised. Highlights • Paragangliomas (PGLs) are slow-growing tumors of neuroendocrine origin.• PGLs in the portocaval region are considered extremely rare.• Their unusual location has its own implications that must be carefully considered.• Clinical findings with imaging techniques and laboratory tests are key to diagnosis.• Surgical resection remains the gold standard of treatment.

SUBMITTER: Ghajar D

PROVIDER: S-EPMC9422283 | biostudies-literature | 2022 Jul

REPOSITORIES: biostudies-literature

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