Ontology highlight
ABSTRACT:
SUBMITTER: Yandow SM
PROVIDER: S-EPMC2841562 | biostudies-other | 2009 May
REPOSITORIES: biostudies-other
Yandow Suzanne M SM Rimoin David L DL Grace Aimee M AM Fillman Ramona R RR Raney Ellen M EM
Journal of pediatric orthopedics. Part B 20090501 3
Treatment of patients with Hutchinson-Gilford progeria syndrome (HGPS) is based on the abnormalities of accelerated aging that affect the healing processes, combined with a fragile cardiovascular status. A classic HGPS case, of Korean ancestry, previously treated for severe coxa valga with bilateral varus osteotomies using blade plate fixation is presented. Complications over the blade plate area required removal of the hardware, after which the patient showed right-sided hypertonicity--determin ...[more]