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Juvenile rheumatic mitral stenosis in association with perimembranous ventricular septal defect in a 3-year-old boy.

ABSTRACT: Rheumatic mitral stenosis (MS) is a well-known entity in the developing world. Though rarely seem, MS can present at a very young age with severe symptoms. We describe here an unusual association of a large perimembranous ventricular septal defect with juvenile rheumatic MS leading to severe pulmonary hypertension and heart failure in a very young child.

SUBMITTER: Vijay SK

PROVIDER: S-EPMC3841425 | biostudies-other | 2013

REPOSITORIES: biostudies-other

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Juvenile rheumatic mitral stenosis in association with perimembranous ventricular septal defect in a 3-year-old boy.

Vijay Sudarshan Kumar SK Tiwari Bhuwan B Misra Mukul M Vijaywargiya Taruna T

BMJ case reports 20131122

Rheumatic mitral stenosis (MS) is a well-known entity in the developing world. Though rarely seem, MS can present at a very young age with severe symptoms. We describe here an unusual association of a large perimembranous ventricular septal defect with juvenile rheumatic MS leading to severe pulmonary hypertension and heart failure in a very young child. ...[more]

PMID: 24273008

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