Unknown

Dataset Information

0

Pulmonary Agenesis and Associated Pulmonary Hypertension: A Case Report and Review on Variability, Therapy, and Outcome.


ABSTRACT: Pulmonary agenesis is a rare congenital disorder with large variability in presentation and prognosis. We describe a full-term infant born with right-sided pulmonary agenesis who underwent thoracoscopic placement of a tissue expander. He ultimately died of pulmonary hypertension. Immunohistology showed intimal hyperplasia without the loss of endothelial caveolin-1 expression. A literature review revealed that while some of these patients have favorable outcome, many succumb despite therapy.

SUBMITTER: Muensterer O 

PROVIDER: S-EPMC4487116 | biostudies-other | 2015 Jun

REPOSITORIES: biostudies-other

Similar Datasets

| S-EPMC7850610 | biostudies-literature
| S-EPMC10248164 | biostudies-literature
| S-EPMC10424440 | biostudies-literature
| S-EPMC4617709 | biostudies-literature
| S-EPMC10463411 | biostudies-literature
| S-EPMC10020523 | biostudies-literature
2024-11-13 | GSE278926 | GEO
| S-EPMC6457075 | biostudies-literature
| S-EPMC5431708 | biostudies-literature