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Correction of Double-Chambered Right Ventricle 40 Years after Pulmonary Valvuloplasty.

ABSTRACT: Background Double-chambered right ventricle is a partial separation of the right ventricle by pathological tissue. This anomaly is described in infants and children but can also be diagnosed in young adults. Case Description A 47-year-old patient presented with chest pain and exercise intolerance. Further evaluation revealed a double-chambered right ventricle. During the surgical procedure, fibrotic tissue was transected, and a pulmonary valve replacement including enlargement of the main pulmonary artery was performed. Conclusion Subpulmonary obstruction of the right ventricle can be related to double-chambered right ventricle even in adulthood. Treatment options include surgical resection with pulmonary valve replacement.

SUBMITTER: Kuhn EW

PROVIDER: S-EPMC4670311 | biostudies-other | 2015 Dec

REPOSITORIES: biostudies-other

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