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Dropped head and man-in-barrel syndrome in amyotrophic lateral sclerosis.

ABSTRACT: We report a case of progressive symmetric brachial weakness followed by cervical muscle weakness. The electromyogram confirmed the diagnosis of amyotrophic lateral sclerosis. After 3 years the patient remained able to walk unassisted and without significant bulbar manifestations or upper neuron signs. The concomitant presence of dropped head syndrome and man-in-barrel syndrome in an amyotrophic lateral sclerosis patient makes our case unique.

SUBMITTER: Almeida R

PROVIDER: S-EPMC5410875 | biostudies-other | 2017 Apr

REPOSITORIES: biostudies-other

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Dropped head and man-in-barrel syndrome in amyotrophic lateral sclerosis.

Almeida Rui R Felix Ana Catarina AC André Ana Luísa AL Nzwalo Hipólito H

Oxford medical case reports 20170404 4

We report a case of progressive symmetric brachial weakness followed by cervical muscle weakness. The electromyogram confirmed the diagnosis of amyotrophic lateral sclerosis. After 3 years the patient remained able to walk unassisted and without significant bulbar manifestations or upper neuron signs. The concomitant presence of dropped head syndrome and man-in-barrel syndrome in an amyotrophic lateral sclerosis patient makes our case unique. ...[more]

PMID: 28473922

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