Ontology highlight
ABSTRACT:
SUBMITTER: Dyck PJ
PROVIDER: S-EPMC5500439 | biostudies-other | 2017 Nov
REPOSITORIES: biostudies-other
Dyck Peter J PJ Kincaid John C JC Dyck P James B PJB Chaudhry Vinay V Goyal Namita A NA Alves Christina C Salhi Hayet H Wiesman Janice F JF Labeyrie Celine C Robinson-Papp Jessica J Cardoso Márcio M Laura Matilde M Ruzhansky Katherine K Cortese Andrea A Brannagan Thomas H TH Khoury Julie J Khella Sami S Waddington-Cruz Márcia M Ferreira João J Wang Annabel K AK Pinto Marcus V MV Ayache Samar S SS Benson Merrill D MD Berk John L JL Coelho Teresa T Polydefkis Michael M Gorevic Peter P Adams David H DH Plante-Bordeneuve Violaine V Whelan Carol C Merlini Giampaolo G Heitner Stephen S Drachman Brian M BM Conceição Isabel I Klein Christopher J CJ Gertz Morie A MA Ackermann Elizabeth J EJ Hughes Steven G SG Mauermann Michelle L ML Bergemann Rito R Lodermeier Karen A KA Davies Jenny L JL Carter Rickey E RE Litchy William J WJ
Muscle & nerve 20170407 5
<h4>Introduction</h4>Polyneuropathy signs (Neuropathy Impairment Score, NIS), neurophysiologic tests (m+7<sub>Ionis</sub> ), disability, and health scores were assessed in baseline evaluations of 100 patients entered into an oligonucleotide familial amyloidotic polyneuropathy (FAP) trial.<h4>Methods</h4>We assessed: (1) Proficiency of grading neurologic signs and correlation with neurophysiologic tests, and (2) clinometric performance of modified NIS+7 neurophysiologic tests (mNIS+7<sub>Ionis</s ...[more]