Pathologically Proven Spontaneous Remission of IgG4-related Retroperitoneal Fibrosis.
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ABSTRACT: Some forms of idiopathic retroperitoneal fibrosis (RF) have recently been considered to be a part of the spectrum of immunoglobulin G4 (IgG4)-related disease. This case report is the first description of a spontaneous remission in a patient with pathologically proven IgG4-related RF. Although the pathogenesis and long-term disease behavior of IgG4-related RF remains unknown, we believe that an initial assessment consisting of only careful monitoring might be one important strategy, especially in asymptomatic IgG4-related RF patients without nephropathy, while carefully monitoring these patients for the risk of recurrence.
SUBMITTER: Yamakawa H
PROVIDER: S-EPMC5548681 | biostudies-other | 2017
REPOSITORIES: biostudies-other
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