Audiometric evaluation in individuals with mucopolysaccharidosis.
Ontology highlight
ABSTRACT:
SUBMITTER: Silveira MRMD
PROVIDER: S-EPMC6251249 | biostudies-other | 2018 Dec
REPOSITORIES: biostudies-other
Publications
Audiometric evaluation in individuals with mucopolysaccharidosis.
Silveira Marcela Rosana Maia da MRMD Buriti Ana Karina Lima AKL Martins Ana Maria AM Gil Daniela D Azevedo Marisa Frasson de MF
Clinics (Sao Paulo, Brazil) 20181203
<h4>Objectives</h4>To characterize the audiometric evaluation and acoustic immittance measures in different types of mucopolysaccharidosis.<h4>Method</h4>Fifty-three mucopolysaccharidosis patients were evaluated. The classification consisted of type I (Hurler syndrome, Hurler-Scheie and Scheie syndrome), type II (Hunter syndrome), type III (Sanfilippo syndrome), type IV (Morquio syndrome), and type VI (Maroteaux-Lamy syndrome). Immittance audiometry and play or conventional threshold tone audiom ...[more]
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