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Bilateral adrenal EBV-associated smooth muscle tumors in a child with a natural killer cell deficiency.

ABSTRACT: EBV-associated smooth muscle tumors are found in immunocompromised patients, most commonly HIV/AIDS. We present a 12-year-old girl with the first documented case of EBV-related smooth muscle tumors in the presence of a rare classic NK cell deficiency. This sheds light on the role of NK cells in controlling EBV-related smooth muscle tumors.

SUBMITTER: Shaw RK

PROVIDER: S-EPMC3350365 | biostudies-literature | 2012 Apr

REPOSITORIES: biostudies-literature

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Bilateral adrenal EBV-associated smooth muscle tumors in a child with a natural killer cell deficiency.

Shaw Rachel K RK Issekutz Andrew C AC Fraser Robert R Schmit Pierre P Morash Barb B Monaco-Shawver Linda L Orange Jordan S JS Fernandez Conrad V CV

Blood 20120316 17

EBV-associated smooth muscle tumors are found in immunocompromised patients, most commonly HIV/AIDS. We present a 12-year-old girl with the first documented case of EBV-related smooth muscle tumors in the presence of a rare classic NK cell deficiency. This sheds light on the role of NK cells in controlling EBV-related smooth muscle tumors. ...[more]

PMID: 22427204

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