Ontology highlight
ABSTRACT:
SUBMITTER: Choi Y
PROVIDER: S-EPMC3945143 | biostudies-literature | 2014 Mar
REPOSITORIES: biostudies-literature
Choi YoungRok Y Yi Nam-Joon NJ Ko Jae Sung JS Ko Jung Min JM Jin Ung Sik US Kim Hee Soo HS Lee Kook Hyun KH Cho Tae-Joon TJ Suh Suk-Won SW Yoo Tae T Lee Kwang-Woong KW Suh Kyung-Suk KS
Journal of Korean medical science 20140227 3
Osteogenesis imperfecta (OI) is a group of genetic disorders characterized by bone fragility and connective tissue manifestations. We report a successful liver transplantation (LT) in an 8-month-old boy with OI and cholestatic biliary cirrhosis. After 4 cycles of intravenous pamidronate, LT was performed under intravenous anesthesia using a left lateral section from his mother without mechanical retractors. The operation time was 420 min and estimated blood loss was 520 mL requiring one unit of ...[more]