Hallervorden-Spatz disease.
Ontology highlight
ABSTRACT:
SUBMITTER: Dashti M
PROVIDER: S-EPMC4190451 | biostudies-literature | 2014
REPOSITORIES: biostudies-literature
Publications
Hallervorden-Spatz disease (HSD) is a rare disorder characterized by progressive extrapyramidal dysfunction and dementia. Hallervorden and Spatz first described the disease, in 1922 as a form of familial brain degeneration characterized by iron deposition in the brain. Here we present four HSD cases with different clinical pictures. ...[more]
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