Syngnathia and obstructive apnea in a case of popliteal pterygium syndrome.
Ontology highlight
ABSTRACT: Unlabelled
We describe an infant with popliteal pterygia, syngnathia, cleft lip and palate, and retrognathia diagnosed with popliteal pterygium syndrome (PPS). The neonatal course was complicated by severe obstructive apnea necessitating tracheostomy.Conclusion
This report illustrates the potential for airway compromise in PPS patients and the need for thorough neonatal airway assessment.
SUBMITTER: Posey JE
PROVIDER: S-EPMC4264642 | biostudies-literature | 2014 Dec
REPOSITORIES: biostudies-literature
Publications
Syngnathia and obstructive apnea in a case of popliteal pterygium syndrome.
Posey Jennifer E JE Dariya Vedanta V Edmonds Joseph L JL Lee Edward I EI Probst Frank J FJ Premkumar Muralidhar H MH
European journal of pediatrics 20141112 12
<h4>Unlabelled</h4>We describe an infant with popliteal pterygia, syngnathia, cleft lip and palate, and retrognathia diagnosed with popliteal pterygium syndrome (PPS). The neonatal course was complicated by severe obstructive apnea necessitating tracheostomy.<h4>Conclusion</h4>This report illustrates the potential for airway compromise in PPS patients and the need for thorough neonatal airway assessment. ...[more]
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